Adenomatoid tumor of the liver presenting as a large multiloculated cyst

Presenter: Sushruta S Nagarkatti MD | Ascension Providence Hospital Background: Adenomatoid tumors are incidentally found, rare that usually benign. They originate from mesothelial cells and have been reported to occur in the genital tract. Occasionally, they extra locations such as adrenal gland, heart, mediastinum, well peritoneal pleural lining. However, liver a primary location for this tumor is extremely rare. Methods: A 33-year-old African-American female with morbid obesity, polycystic ovarian disease, DVT/PE prior cholecystectomy presented right upper quadrant pain. CT scan revealed large multiloculated cystic lesion segments 4 5 of measuring approximately 21.0 x 14.0 cm. The mass extended down into lower quadrant, causing effect effacement duodenum, vena cava displacement transverse colon inferiorly. patient underwent laparoscopic central hepatectomy. Intra-operatively 15 cm neoplasm was found originating extending retroperitoneum. carefully dissected retroperitoneum resected en bloc. Post operatively, did discharged home on post-operative day four. Results: On pathologic analysis, specimen showed multiple cysts variable sizes surrounded by dense stroma mild moderate inflammation. were lined single layer low cuboidal cells. Immunohistochemistry performed staining positive WT-1 calretinin, indicating origin. Second opinion also obtained at tertiary academic center consensus being reached an adenomatoid tumor. Conclusion: origin rarely, if ever primarily liver. Their malignant potential biology unclear due scarcity available literature. Therefore, its treatment surveillance guidelines remain uncertain.